E78.1 Pure hyperglyceridemia
The ICD-10-CM code for Pure hyperglyceridemia is E78.1 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E78
- 24 codes (18 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to E78.1:
- Hyperglyceridemia (endogenous) (essential) (familial) (hereditary) (pure)
- Hypertriglyceridemia, essential
- Hyperprebetalipoproteinemia (familial)
- Prebetalipoproteinemia (acquired) (essential) (familial) (hereditary) (primary) (secondary)
- Very-low-density-lipoprotein-type (VLDL) hyperlipoproteinemia
- Dyslipidemia › elevated fasting triglycerides
- Elevated, elevation › triglycerides
- Elevated, elevation › fasting triglycerides
Inclusion Terms
- Elevated fasting triglycerides
- Endogenous hyperglyceridemia
- Fredrickson's hyperlipoproteinemia, type IV
- Hyperlipidemia, group B
- Hyperprebetalipoproteinemia
- Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia
U.S. Hospital Utilization
- An estimated 151,220 U.S. inpatient stays in 2023 included E78.1 among the documented diagnoses.
- 1,215 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026