E78.011 Heterozygous familial hypercholesterolemia [HeFH]

✓ Billable ICD-10-CM 2026
Open E78.011 in Web App →

The ICD-10-CM code for Heterozygous familial hypercholesterolemia [HeFH] is E78.011 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
E70-E88: Metabolic disorders (E70-E88)
Category E78
24 codes (18 billable)
FY2026 Status
New code in FY2026

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E78.011:

  • HeFH (heterozygous familial hypercholesterolemia)
  • Cholesterolemia (essential) (pure) › familial › heterozygous
  • Hypercholesterolemia (essential) (primary) (pure) › familial › heterozygous [HeFH]

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.a
Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

E78 Disorders of lipoprotein metabolism and other lipidemias

Related Codes in E78

E78 Disorders of lipoprotein metabolism and other lipidemias E78.0 Pure hypercholesterolemia E78.00 Pure hypercholesterolemia, unspecified E78.01 Familial hypercholesterolemia E78.010 Homozygous familial hypercholesterolemia [HoFH] E78.019 Familial hypercholesterolemia, unspecified E78.1 Pure hyperglyceridemia E78.2 Mixed hyperlipidemia E78.3 Hyperchylomicronemia E78.4 Other hyperlipidemia E78.41 Elevated Lipoprotein(a) E78.49 Other hyperlipidemia E78.5 Hyperlipidemia, unspecified E78.6 Lipoprotein deficiency E78.7 Disorders of bile acid and cholesterol metabolism E78.70 Disorder of bile acid and cholesterol metabolism, unspecified E78.71 Barth syndrome E78.72 Smith-Lemli-Opitz syndrome E78.79 Other disorders of bile acid and cholesterol metabolism E78.8 Other disorders of lipoprotein metabolism
Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

Get HCC Mappings, Clinical Summaries, and More

Access premium features including HCC risk adjustment, FDA drug indications, AI coding assistant, and comprehensive clinical context.

Start Free Trial