E75.5 Other lipid storage disorders

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Other lipid storage disorders is E75.5 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
E70-E88: Metabolic disorders (E70-E88)
Category E75
31 codes (26 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E75.5:

  • Wolman's disease
  • Van Bogaert-Scherer-Epstein disease or syndrome
  • Disease, diseased › triglyceride-storage
  • Hyperlipidosis › hereditary NEC
  • Lipidosis › cholesterol (cerebral)
  • Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › cerebrotendinous
  • Cholesterolosis, cholesterosis (gallbladder) › cerebrotendinous
  • Xanthoma (s), xanthomatosis (primary) (familial) (hereditary) › cutaneotendinous

Inclusion Terms

  • Cerebrotendinous cholesterosis [van Bogaert-Scherer-Epstein]
  • Wolman's disease

U.S. Hospital Utilization

  • An estimated 310 U.S. inpatient stays in 2023 included E75.5 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.a
Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Cite This Page

Reference E75.5 with the canonical source and edition:

E75.5 — Other lipid storage disorders. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/E75.5

Canonical URL: https://icd10codingpro.com/codes/E75.5

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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