E75.244 Niemann-Pick disease type A/B

The ICD-10-CM code for Niemann-Pick disease type A/B is E75.244 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E70-E88: Metabolic disorders (E70-E88)

Category E75

31 codes (26 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E75.244:

• Deficiency, deficient › chronic neurovisceral acid sphingomyelinase
• Niemann-Pick disease or syndrome › type › A/B
• Deficiency, deficient › acid sphingomyelinase (ASMD) › type › A/B

Inclusion Terms

• Acid sphingomyelinase deficiency type A/B (ASMD type A/B)
• Chronic neurovisceral acid sphingomyelinase deficiency

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool