E75.24 Niemann-Pick disease
The ICD-10-CM code for Niemann-Pick disease is E75.24 (FY2026). It is a non-billable category code — select a more specific code below for claims.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E75
- 31 codes (26 billable)
- FY2026 Status
- Stable since FY2024
Inclusion Terms
- Acid sphingomyelinase deficiency (ASMD)
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026