E75.3 Sphingolipidosis, unspecified

The ICD-10-CM code for Sphingolipidosis, unspecified is E75.3 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E70-E88: Metabolic disorders (E70-E88)

Category E75

31 codes (26 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E75.3:

• Sphingomyelinosis
• Sphingolipidosis
• Degeneration, degenerative › brain (cortical) (progressive) › in › sphingolipidosis

U.S. Hospital Utilization

E75.3 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference E75.3 with the canonical source and edition:

E75.3 — Sphingolipidosis, unspecified. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/E75.3

Canonical URL: https://icd10codingpro.com/codes/E75.3