E75.29 Other sphingolipidosis

The ICD-10-CM code for Other sphingolipidosis is E75.29 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E70-E88: Metabolic disorders (E70-E88)

Category E75

31 codes (26 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E75.29:

• Farber's disease or syndrome
• Myeloleukodystrophy
• Lipidosis › sulfatide
• Sphingolipidosis › specified NEC
• Aplasia › extracortical axial
• Aplasia › axialis extracorticalis (congenita)
• Lipoid › histiocytosis › essential
• Histiocytosis › lipid, lipoid › essential

Inclusion Terms

• Farber's syndrome
• Sulfatide lipidosis

U.S. Hospital Utilization

• An estimated 1,135 U.S. inpatient stays in 2023 included E75.29 among the documented diagnoses.
• 65 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference E75.29 with the canonical source and edition:

E75.29 — Other sphingolipidosis. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/E75.29

Canonical URL: https://icd10codingpro.com/codes/E75.29