D55.1 Anemia due to other disorders of glutathione metabolism

The ICD-10-CM code for Anemia due to other disorders of glutathione metabolism is D55.1 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Section

D55-D59: Hemolytic anemias (D55-D59)

Category D55

9 codes (7 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D55.1:

• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › erythrocytic glutathione deficiency
• Disorder (of) › pentose phosphate pathway with anemia
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › glutathione-reductase deficiency
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › erythrocytic glutathione
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › 6 phosphogluconate dehydrogenase
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › 6-PGD
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › GGS-R
• Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › deficiency › G SH

Inclusion Terms

• Anemia (due to) enzyme deficiencies, except G6PD, related to the hexose monophosphate [HMP] shunt pathway
• Anemia (due to) hemolytic nonspherocytic (hereditary), type I

U.S. Hospital Utilization

• An estimated 65 U.S. inpatient stays in 2021 included D55.1 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Chapter 3 TOC entry

3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39

Reserved for future guideline expansion

Reserved for future guideline expansion ...................................................................................... 39

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference D55.1 with the canonical source and edition:

D55.1 — Anemia due to other disorders of glutathione metabolism. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/D55.1

Canonical URL: https://icd10codingpro.com/codes/D55.1