Q87.88 CTNNB1 syndrome

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for CTNNB1 syndrome is Q87.88 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q80-Q89: Other congenital malformations (Q80-Q89)
Category Q87
25 codes (20 billable)
FY2026 Status
New code in FY2026

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q87.88:

  • Syndrome › CTNNB1
Use Additional Code
  • code, if applicable, for associated conditions such as:
  • cerebral palsy (G80.-)
  • congenital heart malformations (Q20.0-Q24.9)
  • developmental disorder of speech and language (F80.-)
  • exudative retinopathy (H35.02-)
  • intellectual disability (F70-F79)
  • microcephaly (Q02)

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

Q87 Other specified congenital malformation syndromes affecting multiple systems

Related Codes in Q87

Q87 Other specified congenital malformation syndromes affecting multiple systems Q87.0 Congenital malformation syndromes predominantly affecting facial appearance Q87.1 Congenital malformation syndromes predominantly associated with short stature Q87.11 Prader-Willi syndrome Q87.19 Other congenital malformation syndromes predominantly associated with short stature Q87.2 Congenital malformation syndromes predominantly involving limbs Q87.3 Congenital malformation syndromes involving early overgrowth Q87.4 Marfan syndrome Q87.40 Marfan syndrome, unspecified Q87.41 Marfan syndrome with cardiovascular manifestations Q87.410 Marfan syndrome with aortic dilation Q87.418 Marfan syndrome with other cardiovascular manifestations Q87.42 Marfan syndrome with ocular manifestations Q87.43 Marfan syndrome with skeletal manifestation Q87.5 Other congenital malformation syndromes with other skeletal changes Q87.8 Other specified congenital malformation syndromes, not elsewhere classified Q87.81 Alport syndrome Q87.82 Arterial tortuosity syndrome Q87.83 Bardet-Biedl syndrome Q87.84 Laurence-Moon syndrome
Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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