Q87.418 Marfan syndrome with other cardiovascular manifestations

The ICD-10-CM code for Marfan syndrome with other cardiovascular manifestations is Q87.418 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

17: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Section

Q80-Q89: Other congenital malformations (Q80-Q89)

Category Q87

25 codes (20 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q87.418:

• Syndrome › Marfan › with › cardiovascular manifestations

U.S. Hospital Utilization

• An estimated 970 U.S. inpatient stays in 2023 included Q87.418 among the documented diagnoses.
• 100 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference Q87.418 with the canonical source and edition:

Q87.418 — Marfan syndrome with other cardiovascular manifestations. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/Q87.418

Canonical URL: https://icd10codingpro.com/codes/Q87.418