Q87.4 Marfan syndrome

⚠ Non-Billable ICD-10-CM 2026
Open Q87.4 in Web App →

The ICD-10-CM code for Marfan syndrome is Q87.4 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Section
Q80-Q89: Other congenital malformations (Q80-Q89)
Category Q87
25 codes (20 billable)
FY2026 Status
Stable since FY2024

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

Q87 Other specified congenital malformation syndromes affecting multiple systems

More Specific Codes

Q87.40 Marfan syndrome, unspecified Q87.41 Marfan syndrome with cardiovascular manifestations Q87.410 Marfan syndrome with aortic dilation Q87.418 Marfan syndrome with other cardiovascular manifestations Q87.42 Marfan syndrome with ocular manifestations Q87.43 Marfan syndrome with skeletal manifestation

Related Codes in Q87

Q87 Other specified congenital malformation syndromes affecting multiple systems Q87.0 Congenital malformation syndromes predominantly affecting facial appearance Q87.1 Congenital malformation syndromes predominantly associated with short stature Q87.11 Prader-Willi syndrome Q87.19 Other congenital malformation syndromes predominantly associated with short stature Q87.2 Congenital malformation syndromes predominantly involving limbs Q87.3 Congenital malformation syndromes involving early overgrowth Q87.40 Marfan syndrome, unspecified Q87.41 Marfan syndrome with cardiovascular manifestations Q87.410 Marfan syndrome with aortic dilation Q87.418 Marfan syndrome with other cardiovascular manifestations Q87.42 Marfan syndrome with ocular manifestations Q87.43 Marfan syndrome with skeletal manifestation Q87.5 Other congenital malformation syndromes with other skeletal changes Q87.8 Other specified congenital malformation syndromes, not elsewhere classified Q87.81 Alport syndrome Q87.82 Arterial tortuosity syndrome Q87.83 Bardet-Biedl syndrome Q87.84 Laurence-Moon syndrome Q87.85 MED13L syndrome
Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

Get HCC Mappings, Clinical Summaries, and More

Access premium features including HCC risk adjustment, FDA drug indications, AI coding assistant, and comprehensive clinical context.

Start Free Trial