I01 Rheumatic fever with heart involvement

The ICD-10-CM code for Rheumatic fever with heart involvement is I01 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Chapter

9: Diseases of the circulatory system (I00-I99)

Section

I00-I02: Acute rheumatic fever (I00-I02)

Category I01

6 codes (5 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to I01:

• Fever (inanition) (of unknown origin) (persistent) (with chills) (with rigor) › rheumatic (active) (acute) (chronic) (subacute) › active with heart involvement

Official Coding Guidelines

Presumed relationship due to Index term “with”

The classification presumes a causal relationship between hypertension and heart involvement and between hypertension and kidney involvement, as the two conditions are linked by the term “with” in the Alphabetic Index. These conditions should be coded as related even in the absence of provider documentation explicitly linking them, unless the documentation clearly states the conditions are unrelated.

Provider must link conditions not specifically indexed as related

For hypertension and conditions not specifically linked by relational terms such as “with,” “associated with” or “due to” in the classification, provider documentation must link the conditions in order to code them as related.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool

Cite This Page

Reference I01 with the canonical source and edition:

I01 — Rheumatic fever with heart involvement. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/I01

Canonical URL: https://icd10codingpro.com/codes/I01