I01.9 Acute rheumatic heart disease, unspecified
The ICD-10-CM code for Acute rheumatic heart disease, unspecified is I01.9 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- I00-I02: Acute rheumatic fever (I00-I02)
- Category I01
- 6 codes (5 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to I01.9:
- Bouillaud's disease or syndrome (rheumatic heart disease)
- Disease, diseased › Bouillaud's (rheumatic heart disease)
- Syndrome › Bouillaud's
- Disease, diseased › heart (organic) › rheumatic (chronic) (inactive) (old) (quiescent) (with chorea) › active or acute
- Disease, diseased › heart (organic) › with › rheumatic fever (conditions in I00) › active
Inclusion Terms
- Any condition in I00 with unspecified type of heart involvement
- Rheumatic carditis, acute
- Rheumatic heart disease, active or acute
U.S. Hospital Utilization
- An estimated 55 U.S. inpatient stays in 2016 included I01.9 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Presumed relationship due to Index term “with”The classification presumes a causal relationship between hypertension and heart involvement and between hypertension and kidney involvement, as the two conditions are linked by the term “with” in the Alphabetic Index. These conditions should be coded as related even in the absence of provider documentation explicitly linking them, unless the documentation clearly states the conditions are unrelated.
Provider must link conditions not specifically indexed as relatedFor hypertension and conditions not specifically linked by relational terms such as “with,” “associated with” or “due to” in the classification, provider documentation must link the conditions in order to code them as related.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026