G12.1 Other inherited spinal muscular atrophy

The ICD-10-CM code for Other inherited spinal muscular atrophy is G12.1 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G10-G14: Systemic atrophies primarily affecting the central nervous system (G10-G14)

Category G12

13 codes (11 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G12.1:

• Fazio-Londe disease or syndrome
• Kugelberg-Welander disease
• Palsy › bulbar (progressive) (chronic) › of childhood (Fazio-Londe)
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › progressive (bulbar) › adult
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › hereditary NEC
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › adult form
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › distal
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › childhood form, type II

Inclusion Terms

• Adult form spinal muscular atrophy
• Childhood form, type II spinal muscular atrophy
• Distal spinal muscular atrophy
• Juvenile form, type III spinal muscular atrophy [Kugelberg-Welander]
• Progressive bulbar palsy of childhood [Fazio-Londe]
• Scapuloperoneal form spinal muscular atrophy

U.S. Hospital Utilization

• An estimated 650 U.S. inpatient stays in 2023 included G12.1 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)