G12.0 Infantile spinal muscular atrophy, type I [Werdnig-Hoffman]

The ICD-10-CM code for Infantile spinal muscular atrophy, type I [Werdnig-Hoffman] is G12.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G10-G14: Systemic atrophies primarily affecting the central nervous system (G10-G14)

Category G12

13 codes (11 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G12.0:

• Werdnig-Hoffmann syndrome (muscular atrophy)
• Syndrome › Werdnig-Hoffman
• Disease, diseased › Werdnig-Hoffmann
• Atrophy, atrophic (of) › Werdnig-Hoffmann
• Syndrome › Hoffmann-Werdnig
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › infantile spinal
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › spinal › infantile, type I (Werdnig-Hoffmann)
• Atrophy, atrophic (of) › muscle, muscular (diffuse) (general) (idiopathic) (primary) › progressive (bulbar) › infantile (spinal)

U.S. Hospital Utilization

• An estimated 750 U.S. inpatient stays in 2023 included G12.0 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)