D81.82 Activated Phosphoinositide 3-kinase Delta Syndrome [APDS]

✓ Billable ICD-10-CM 2026
Open D81.82 in Web App →

The ICD-10-CM code for Activated Phosphoinositide 3-kinase Delta Syndrome [APDS] is D81.82 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
D80-D89: Certain disorders involving the immune mechanism (D80-D89)
Category D81
21 codes (17 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D81.82:

  • Syndrome › activated phosphoinositide 3-kinase delta syndrome [APDS]
  • Disease, diseased › p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI]
Code Also
  • , if applicable, any associated manifestations, such as:
  • bronchiectasis (J47.-)
  • herpes virus infections (B00.-)
  • other acute respiratory tract infections (J00-J06; J20-J22)
  • other infections (A00-B99)
  • pneumonia (J12-J18)

Inclusion Terms

  • p110d-activating mutation causing senescent T cells, lymphadenopathy, and immunodeficiency [PASLI] disease

U.S. Hospital Utilization

D81.82 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Chapter 3 TOC entry

3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.3
Reserved for future guideline expansion

Reserved for future guideline expansion ...................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.3.Reserved

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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