D56.1 Beta thalassemia
The ICD-10-CM code for Beta thalassemia is D56.1 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- D55-D59: Hemolytic anemias (D55-D59)
- Category D56
- 9 codes (8 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to D56.1:
- Cooley's anemia
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › Cooley's (erythroblastic)
- Thalassemia (anemia) (disease) › major
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › familial erythroblastic
- Thalassemia (anemia) (disease) › beta (severe)
- Thalassemia (anemia) (disease) › intermedia
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › erythroblastic › familial
- Anemia (essential) (general) (hemoglobin deficiency) (infantile) (primary) (profound) › erythroblastic › of childhood
Inclusion Terms
- Beta thalassemia major
- Cooley's anemia
- Homozygous beta thalassemia
- Severe beta thalassemia
- Thalassemia intermedia
- Thalassemia major
U.S. Hospital Utilization
- An estimated 7,265 U.S. inpatient stays in 2023 included D56.1 among the documented diagnoses.
- 410 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Chapter 3 TOC entry3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39
Reserved for future guideline expansionReserved for future guideline expansion ...................................................................................... 39
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026