D56.0 Alpha thalassemia
The ICD-10-CM code for Alpha thalassemia is D56.0 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- D55-D59: Hemolytic anemias (D55-D59)
- Category D56
- 9 codes (8 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to D56.0:
- Hb (abnormal) › Bart's disease
- Thalassemia (anemia) (disease) › alpha (major) (severe) (triple gene defect)
- Hemoglobin › H Constant Spring
- Disease, diseased › hemoglobin or Hb › Bart's
- Disease, diseased › hemoglobin or Hb › H (Hb-H) (thalassemia)
- Hydrops › newborn (idiopathic) › due to › alpha thalassemia
- Disease, diseased › hemoglobin or Hb › H (Hb-H) (thalassemia) › Constant Spring
- Hydrops › fetalis › due to › alpha thalassemia
Inclusion Terms
- Alpha thalassemia major
- Hemoglobin H Constant Spring
- Hemoglobin H disease
- Hydrops fetalis due to alpha thalassemia
- Severe alpha thalassemia
- Triple gene defect alpha thalassemia
U.S. Hospital Utilization
- An estimated 4,795 U.S. inpatient stays in 2023 included D56.0 among the documented diagnoses.
- 80 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Chapter 3 TOC entry3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39
Reserved for future guideline expansionReserved for future guideline expansion ...................................................................................... 39
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026