Q89.3 Situs inversus
The ICD-10-CM code for Situs inversus is Q89.3 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q80-Q89: Other congenital malformations (Q80-Q89)
- Category Q89
- 13 codes (10 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q89.3:
- Situs inversus or transversus (abdominalis) (thoracis)
- Kartagener's syndrome or triad (sinusitis, bronchiectasis, situs inversus)
- Sinusitis-bronchiectasis-situs inversus (syndrome) (triad)
- Syndrome › sinusitis-bronchiectasis-situs inversus
- Transposition (congenital) › viscera (abdominal) (thoracic)
- Syndrome › Kartagener's
- Levocardia (isolated) › with situs inversus
- Transposition (congenital) › abdominal viscera
Inclusion Terms
- Dextrocardia with situs inversus
- Mirror-image atrial arrangement with situs inversus
- Situs inversus or transversus abdominalis
- Situs inversus or transversus thoracis
- Transposition of abdominal viscera
- Transposition of thoracic viscera
U.S. Hospital Utilization
- An estimated 3,595 U.S. inpatient stays in 2023 included Q89.3 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026