Q89.09 Congenital malformations of spleen
The ICD-10-CM code for Congenital malformations of spleen is Q89.09 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q80-Q89: Other congenital malformations (Q80-Q89)
- Category Q89
- 13 codes (10 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q89.09:
- Polysplenia syndrome
- Ectopic, ectopia (congenital) › spleen
- Aberrant (congenital) › spleen
- Anomaly, anomalous (congenital) (unspecified type) › spleen
- Distortion (s) (congenital) › spleen
- Displacement, displaced › spleen (congenital)
- Lobulation (congenital) › spleen
- Accessory (congenital) › spleen
Inclusion Terms
- Congenital splenomegaly
U.S. Hospital Utilization
- An estimated 2,250 U.S. inpatient stays in 2023 included Q89.09 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026