Q89.09 Congenital malformations of spleen

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Congenital malformations of spleen is Q89.09 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q80-Q89: Other congenital malformations (Q80-Q89)
Category Q89
13 codes (10 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q89.09:

  • Polysplenia syndrome
  • Ectopic, ectopia (congenital) › spleen
  • Aberrant (congenital) › spleen
  • Anomaly, anomalous (congenital) (unspecified type) › spleen
  • Distortion (s) (congenital) › spleen
  • Displacement, displaced › spleen (congenital)
  • Lobulation (congenital) › spleen
  • Accessory (congenital) › spleen

Inclusion Terms

  • Congenital splenomegaly

U.S. Hospital Utilization

  • An estimated 2,250 U.S. inpatient stays in 2023 included Q89.09 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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