Q80.8 Other congenital ichthyosis
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The ICD-10-CM code for Other congenital ichthyosis is Q80.8 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q80-Q89: Other congenital malformations (Q80-Q89)
- Category Q80
- 8 codes (7 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q80.8:
- Ichthyosis (congenital) › hystrix
- Ichthyosis (congenital) › vera
- Keratosis › congenital, specified NEC
- Hyperkeratosis › universalis congenita
U.S. Hospital Utilization
- An estimated 90 U.S. inpatient stays in 2023 included Q80.8 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026
References
Cite This Page
Reference Q80.8 with the canonical source and edition:
Q80.8 — Other congenital ichthyosis. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/Q80.8
Canonical URL: https://icd10codingpro.com/codes/Q80.8