Q41 Congenital absence, atresia and stenosis of small intestine

⚠ Non-Billable ICD-10-CM 2026
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The ICD-10-CM code for Congenital absence, atresia and stenosis of small intestine is Q41 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Section
Q38-Q45: Other congenital malformations of the digestive system (Q38-Q45)
Category Q41
6 codes (5 billable)
FY2026 Status
Stable since FY2024
Includes
  • congenital obstruction, occlusion or stricture of small intestine or intestine NOS
Excludes1
Not coded here. These conditions should NOT be coded together with Q41.
  • cystic fibrosis with intestinal manifestation (E84.11)
  • meconium ileus NOS (without cystic fibrosis) (P76.0)

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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