Q01 Encephalocele

⚠ Non-Billable ICD-10-CM 2026
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The ICD-10-CM code for Encephalocele is Q01 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Section
Q00-Q07: Congenital malformations of the nervous system (Q00-Q07)
Category Q01
6 codes (5 billable)
FY2026 Status
Stable since FY2024
Includes
  • Arnold-Chiari syndrome, type III
  • encephalocystocele
  • encephalomyelocele
  • hydroencephalocele
  • hydromeningocele, cranial
  • meningocele, cerebral
  • meningoencephalocele
Excludes1
Not coded here. These conditions should NOT be coded together with Q01.
  • Meckel-Gruber syndrome (Q61.9)

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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