G71.3 Mitochondrial myopathy, not elsewhere classified

✓ Billable HCC ICD-10-CM 2026

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The ICD-10-CM code for Mitochondrial myopathy, not elsewhere classified is G71.3 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
G70-G73: Diseases of myoneural junction and muscle (G70-G73)
Category G71
35 codes (28 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G71.3:

  • Myopathy › mitochondrial NEC
Excludes1
Not coded here. These conditions should NOT be coded together with G71.3.
  • Kearns-Sayre syndrome (H49.81)
  • Leber's disease (H47.21)
  • Leigh's encephalopathy (G31.82)
  • mitochondrial metabolism disorders (E88.4.-)
  • Reye's syndrome (G93.7)

U.S. Hospital Utilization

  • An estimated 960 U.S. inpatient stays in 2023 included G71.3 among the documented diagnoses.
  • 65 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.6.a
Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.6.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Cite This Page

Reference G71.3 with the canonical source and edition:

G71.3 — Mitochondrial myopathy, not elsewhere classified. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/G71.3

Canonical URL: https://icd10codingpro.com/codes/G71.3

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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