G71.032 Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction

The ICD-10-CM code for Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction is G71.032 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G70-G73: Diseases of myoneural junction and muscle (G70-G73)

Category G71

35 codes (28 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G71.032:

• Calpainopathy (primary)
• Calpainopathy (primary) › autosomal recessive
• Dystrophy, dystrophia › Leyden-Möbius › meaning Limb girdle muscular dystrophy type 2A (autosomal recessive)
• Dystrophy, dystrophia › muscular › limb-girdle › calpain-3-related
• Dystrophy, dystrophia › muscular › limb-girdle › type 2A (autosomal recessive)
• Dystrophy, dystrophia › muscular › limb-girdle › R1 (autosomal recessive)
• Dystrophy, dystrophia › muscular › limb-girdle › calpain-3-related › autosomal recessive

Inclusion Terms

• Limb girdle muscular dystrophy type 2A
• LGMD R1 calpain-3-related
• Primary calpainopathy

U.S. Hospital Utilization

G71.032 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference G71.032 with the canonical source and edition:

G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/G71.032

Canonical URL: https://icd10codingpro.com/codes/G71.032