G40.42 Cyclin-Dependent Kinase-Like 5 Deficiency Disorder

The ICD-10-CM code for Cyclin-Dependent Kinase-Like 5 Deficiency Disorder is G40.42 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

6: Diseases of the nervous system (G00-G99)

Section

G40-G47: Episodic and paroxysmal disorders (G40-G47)

Category G40

94 codes (58 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G40.42:

• CDKL5 (Cyclin-Dependent Kinase-Like 5 Deficiency Disorder)
• Disorder (of) › Cyclin-Dependent Kinase-Like 5 Deficiency (CDKL5)

Inclusion Terms

• CDKL5

U.S. Hospital Utilization

• An estimated 225 U.S. inpatient stays in 2023 included G40.42 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference G40.42 with the canonical source and edition:

G40.42 — Cyclin-Dependent Kinase-Like 5 Deficiency Disorder. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/G40.42

Canonical URL: https://icd10codingpro.com/codes/G40.42