What is the ICD-10 code for Huntington's disease?

The ICD-10-CM code for Huntington's disease is G10 (fiscal year 2026). It is a billable diagnosis code.

What does ICD-10 code G10 mean?

G10 is the ICD-10-CM diagnosis code for Huntington's disease. Huntington's disease

Is G10 a billable ICD-10 code?

Yes, G10 is a billable ICD-10-CM code that can be used on medical claims.

What chapter is G10 in?

G10 is classified under Chapter 6: Diseases of the nervous system (G00-G99), Section G10-G14: Systemic atrophies primarily affecting the central nervous system (G10-G14).

G10 Huntington's disease

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The ICD-10-CM code for Huntington's disease is G10 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter: 6: Diseases of the nervous system (G00-G99)
Section: G10-G14: Systemic atrophies primarily affecting the central nervous system (G10-G14)
Category G10: 1 code (1 billable)
FY2026 Status: Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to G10:

Huntington's disease or chorea
Huntington's disease or chorea › with dementia
Chorea (chronic) (gravis) (posthemiplegic) (senile) (spasmodic) › hereditary
Chorea (chronic) (gravis) (posthemiplegic) (senile) (spasmodic) › Huntington's
Disease, diseased › Huntington's
Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) › in (due to) › Huntington's disease or chorea
Disease, diseased › Huntington's › with dementia
Chorea (chronic) (gravis) (posthemiplegic) (senile) (spasmodic) › progressive › hereditary

Use Additional Code

code, if applicable, to identify:
dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4)
dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-)
dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3)
dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2)
dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0)
mild neurocognitive disorder due to known physiological condition (F06.7-)

Inclusion Terms

Huntington's chorea
Huntington's dementia

U.S. Hospital Utilization

An estimated 4,830 U.S. inpatient stays in 2023 included G10 among the documented diagnoses.
570 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Dominant/nondominant side (TOC entry)

a. Dominant/nondominant side ................................................................................................. 45

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.6.a

Pain - Category G89 (TOC entry)

b. Pain - Category G89.............................................................................................................. 45

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.6.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026