E83.822 ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2

The ICD-10-CM code for ENPP1 deficiency causing autosomal recessive hypophosphatemic rickets type 2 is E83.822 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E70-E88: Metabolic disorders (E70-E88)

Category E83

40 codes (31 billable)

FY2026 Status

New code in FY2026

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E83.822:

• Deficiency, deficient › ENPP1 › causing › autosomal recessive hypophosphatemic rickets type 2

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool