E83.01 Wilson's disease

The ICD-10-CM code for Wilson's disease is E83.01 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

4: Endocrine, nutritional and metabolic diseases (E00-E89)

Section

E70-E88: Metabolic disorders (E70-E88)

Category E83

40 codes (31 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E83.01:

• Kinnier Wilson's disease (hepatolenticular degeneration)
• Lenticular degeneration, progressive
• Hepatolenticular degeneration
• Strümpell-Westphal pseudosclerosis
• Westphal-Strümpell syndrome
• Deficiency, deficient › ceruloplasmin (Wilson)
• Degeneration, degenerative › hepatolenticular (Wilson's)
• Degeneration, degenerative › lenticular (familial) (progressive) (Wilson's) (with cirrhosis of liver)

U.S. Hospital Utilization

• An estimated 1,520 U.S. inpatient stays in 2023 included E83.01 among the documented diagnoses.
• 80 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)