E74.09 Other glycogen storage disease
The ICD-10-CM code for Other glycogen storage disease is E74.09 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E74
- 32 codes (24 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to E74.09:
- Andersen's disease (glycogen storage)
- Tauri's disease
- Hers' disease
- Deficiency, deficient › phosphorylase kinase, liver
- Deficiency, deficient › hepatophosphorylase
- Deficiency, deficient › liver phosphorylase
- Deficiency, deficient › glycogen synthetase
- Disease, diseased › Andersen's (glycogenosis IV)
Inclusion Terms
- Andersen disease
- Glycogen storage disease, types 0, IV, VI-XI
- Hers disease
- Liver phosphorylase deficiency
- Muscle phosphofructokinase deficiency
- Tauri disease
U.S. Hospital Utilization
- An estimated 185 U.S. inpatient stays in 2023 included E74.09 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026