E74.03 Cori disease
The ICD-10-CM code for Cori disease is E74.03 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E74
- 32 codes (24 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to E74.03:
- Forbes' glycogen storage disease
- Cori's disease (glycogen storage)
- Amylopectinosis (brancher enzyme deficiency)
- Dextrinosis, limit (debrancher enzyme deficiency)
- Deficiency, deficient › brancher enzyme (amylopectinosis)
- Disease, diseased › Cori's (glycogenosis III)
- Deficiency, deficient › debrancher enzyme (limit dextrinosis)
- Disease, diseased › Forbes' (glycogenosis III)
Inclusion Terms
- Forbes disease
- Type III glycogen storage disease
U.S. Hospital Utilization
- An estimated 95 U.S. inpatient stays in 2023 included E74.03 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026