E72.19 Other disorders of sulfur-bearing amino-acid metabolism

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Other disorders of sulfur-bearing amino-acid metabolism is E72.19 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
E70-E88: Metabolic disorders (E70-E88)
Category E72
39 codes (31 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to E72.19:

  • Hypermethioninemia
  • Methioninemia
  • Cystathioninuria
  • Cystathioninemia
  • Deficiency, deficient › sulfite oxidase
  • Malabsorption › methionine
  • Disease, diseased › oast-house-urine
  • Disorder (of) › amino-acid › cystathioninuria

Inclusion Terms

  • Cystathioninuria
  • Methioninemia
  • Sulfite oxidase deficiency

U.S. Hospital Utilization

  • An estimated 65 U.S. inpatient stays in 2022 included E72.19 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.a
Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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