E71.541 Zellweger-like syndrome
E71.541 is a risk-adjusting diagnosis under CMS-HCC and RxHCC models. Create a free account to see model versions, RAF contribution, and AI-powered HCC suppression analysis.
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The ICD-10-CM code for Zellweger-like syndrome is E71.541 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E71
- 50 codes (38 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to E71.541:
- Syndrome › Zellweger-like syndrome
- Disorder (of) › peroxisomal › Zellweger-like syndrome
U.S. Hospital Utilization
E71.541 appeared in too few sampled U.S. inpatient stays in 2021 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026
References
Cite This Page
Reference E71.541 with the canonical source and edition:
E71.541 — Zellweger-like syndrome. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/E71.541
Canonical URL: https://icd10codingpro.com/codes/E71.541