E71.51 Disorders of peroxisome biogenesis

⚠ Non-Billable ICD-10-CM 2026
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The ICD-10-CM code for Disorders of peroxisome biogenesis is E71.51 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Section
E70-E88: Metabolic disorders (E70-E88)
Category E71
50 codes (38 billable)
FY2026 Status
Stable since FY2024
Excludes1
Not coded here. These conditions should NOT be coded together with E71.51.
  • Refsum's disease (G60.1)

Inclusion Terms

  • Group 1 peroxisomal disorders

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.a
Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Cite This Page

Reference E71.51 with the canonical source and edition:

E71.51 — Disorders of peroxisome biogenesis. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/E71.51

Canonical URL: https://icd10codingpro.com/codes/E71.51

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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