E71.3 Disorders of fatty-acid metabolism

⚠ Non-Billable ICD-10-CM 2026
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The ICD-10-CM code for Disorders of fatty-acid metabolism is E71.3 (FY2026). It is a non-billable category code — select a more specific code below for claims.

Classification

Section
E70-E88: Metabolic disorders (E70-E88)
Category E71
50 codes (38 billable)
FY2026 Status
Stable since FY2024
Excludes1
Not coded here. These conditions should NOT be coded together with E71.3.
  • peroxisomal disorders (E71.5)
  • Refsum's disease (G60.1)
  • Schilder's disease (G37.0)
Excludes2
Not included here. These conditions are coded elsewhere but may be coded together if applicable.
  • carnitine deficiency due to inborn error of metabolism (E71.42)

Official Coding Guidelines

Diabetes mellitus (TOC entry)

a. Diabetes mellitus ................................................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.a
Obesity (TOC entry)

b. Obesity .................................................................................................................................. 42

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.4.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Parent Code

E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism

More Specific Codes

E71.30 Disorder of fatty-acid metabolism, unspecified E71.31 Disorders of fatty-acid oxidation E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency E71.311 Medium chain acyl CoA dehydrogenase deficiency E71.312 Short chain acyl CoA dehydrogenase deficiency E71.313 Glutaric aciduria type II E71.314 Muscle carnitine palmitoyltransferase deficiency E71.318 Other disorders of fatty-acid oxidation E71.32 Disorders of ketone metabolism E71.39 Other disorders of fatty-acid metabolism

Related Codes in E71

E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism E71.0 Maple-syrup-urine disease E71.1 Other disorders of branched-chain amino-acid metabolism E71.11 Branched-chain organic acidurias E71.110 Isovaleric acidemia E71.111 3-methylglutaconic aciduria E71.118 Other branched-chain organic acidurias E71.12 Disorders of propionate metabolism E71.120 Methylmalonic acidemia E71.121 Propionic acidemia E71.128 Other disorders of propionate metabolism E71.19 Other disorders of branched-chain amino-acid metabolism E71.2 Disorder of branched-chain amino-acid metabolism, unspecified E71.30 Disorder of fatty-acid metabolism, unspecified E71.31 Disorders of fatty-acid oxidation E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency E71.311 Medium chain acyl CoA dehydrogenase deficiency E71.312 Short chain acyl CoA dehydrogenase deficiency E71.313 Glutaric aciduria type II E71.314 Muscle carnitine palmitoyltransferase deficiency
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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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