E71.19 Other disorders of branched-chain amino-acid metabolism
The ICD-10-CM code for Other disorders of branched-chain amino-acid metabolism is E71.19 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- E70-E88: Metabolic disorders (E70-E88)
- Category E71
- 50 codes (38 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to E71.19:
- Hyperleucine-isoleucinemia
- Isoleucinosis
- Hypervalinemia
- Hypoglycemia (spontaneous) › leucine-induced
- Disorder (of) › hyperleucine-isoleucinemia
- Disorder (of) › hypervalinemia
- Disorder (of) › metabolism NOS › isoleucine
- Disorder (of) › branched-chain amino-acid metabolism › specified NEC
Inclusion Terms
- Hyperleucine-isoleucinemia
- Hypervalinemia
U.S. Hospital Utilization
- An estimated 195 U.S. inpatient stays in 2023 included E71.19 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Diabetes mellitus (TOC entry)a. Diabetes mellitus ................................................................................................................... 39
Obesity (TOC entry)b. Obesity .................................................................................................................................. 42
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026