D74.0 Congenital methemoglobinemia

The ICD-10-CM code for Congenital methemoglobinemia is D74.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

3: Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89)

Section

D70-D77: Other disorders of blood and blood-forming organs (D70-D77)

Category D74

4 codes (3 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D74.0:

• Disease, diseased › diaphorase deficiency
• Deficiency, deficient › NADH diaphorase or reductase (congenital)
• Methemoglobinemia › enzymatic (congenital)
• Deficiency, deficient › NADH-methemoglobin reductase (congenital)
• Methemoglobinemia › Hb M disease
• Methemoglobinemia › congenital
• Methemoglobinemia › hereditary
• Disease, diseased › hemoglobin or Hb › M

Inclusion Terms

• Congenital NADH-methemoglobin reductase deficiency
• Hemoglobin-M [Hb-M] disease
• Methemoglobinemia, hereditary

U.S. Hospital Utilization

• An estimated 80 U.S. inpatient stays in 2023 included D74.0 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Chapter 3 TOC entry

3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39

Reserved for future guideline expansion

Reserved for future guideline expansion ...................................................................................... 39

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)

Cite This Page

Reference D74.0 with the canonical source and edition:

D74.0 — Congenital methemoglobinemia. ICD-10 Coding Pro (ICD-10-CM FY2026). https://icd10codingpro.com/codes/D74.0

Canonical URL: https://icd10codingpro.com/codes/D74.0