D68.1 Hereditary factor XI deficiency
The ICD-10-CM code for Hereditary factor XI deficiency is D68.1 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- D65-D69: Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
- Category D68
- 32 codes (25 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to D68.1:
- Rosenthal's disease or syndrome
- Disease, diseased › Rosenthal's (factor XI deficiency)
- Hemophilia (classical) (familial) (hereditary) › C
- Deficiency, deficient › PTA (plasma thromboplastin antecedent)
- Deficiency, deficient › plasma thromboplastin › antecedent (PTA)
- Deficiency, deficient › factor › XI (congenital) (hereditary)
- Deficiency, deficient › anti-hemophilic › factor (A) › C
Inclusion Terms
- Hemophilia C
- Plasma thromboplastin antecedent [PTA] deficiency
- Rosenthal's disease
U.S. Hospital Utilization
- An estimated 2,030 U.S. inpatient stays in 2023 included D68.1 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Chapter 3 TOC entry3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39
Reserved for future guideline expansionReserved for future guideline expansion ...................................................................................... 39
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026