D65 Disseminated intravascular coagulation [defibrination syndrome]

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Disseminated intravascular coagulation [defibrination syndrome] is D65 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
D65-D69: Coagulation defects, purpura and other hemorrhagic conditions (D65-D69)
Category D65
1 code (1 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D65:

  • Defibrination (syndrome)
  • Proteolysis, pathologic
  • Fibrinolysis (hemorrhagic) (acquired)
  • Coagulation, intravascular (diffuse) (disseminated) › COVID-19 associated
  • Coagulopathy › consumption
  • Coagulopathy › intravascular
  • Fibrinogenopenia › acquired
  • Afibrinogenemia › acquired
Excludes1
Not coded here. These conditions should NOT be coded together with D65.
  • disseminated intravascular coagulation (complicating):
  • in newborn (P60)
  • pregnancy, childbirth and the puerperium (O45.0, O46.0, O67.0, O72.3)
Excludes2
Not included here. These conditions are coded elsewhere but may be coded together if applicable.
  • disseminated intravascular coagulation (complicating):
  • abortion or ectopic or molar pregnancy (O00-O07, O08.1)
Code Also
  • , if applicable, associated condition

Inclusion Terms

  • Afibrinogenemia, acquired
  • Consumption coagulopathy
  • COVID-19 associated diffuse or disseminated intravascular coagulopathy
  • Diffuse or disseminated intravascular coagulation [DIC]
  • Fibrinolytic hemorrhage, acquired
  • Fibrinolytic purpura
  • Purpura fulminans

U.S. Hospital Utilization

  • An estimated 45,520 U.S. inpatient stays in 2023 included D65 among the documented diagnoses.
  • 585 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Chapter 3 TOC entry

3. Chapter 3: Disease of the blood and blood-forming organs and certain disorders involving the immune mechanism (D50-D89) ............................................................................................. 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.3
Reserved for future guideline expansion

Reserved for future guideline expansion ...................................................................................... 39

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.3.Reserved

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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