D47.02 Systemic mastocytosis

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Systemic mastocytosis is D47.02 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
D37-D48: Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48)
Category D47
14 codes (11 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D47.02:

  • Disease, diseased › systemic tissue mast cell
  • Mastocytosis › isolated bone marrow
  • Mast cell › disease, systemic tissue
  • Mastocytosis › indolent systemic
  • Mastocytosis › systemic (indolent) (smoldering) › with an associated hematological non-mast cell lineage disease (SM-AHNMD)
Excludes1
Not coded here. These conditions should NOT be coded together with D47.02.
  • aggressive systemic mastocytosis (C96.21)
  • mast cell leukemia (C94.3-)
Code Also
  • , if applicable, any associated hematological non-mast cell lineage disease, such as:
  • acute myeloid leukemia (C92.6-, C92.A-)
  • chronic myelomonocytic leukemia (C93.1-)
  • essential thrombocytosis (D47.3)
  • hypereosinophilic syndrome (D72.1)
  • myelodysplastic syndrome (D46.9)
  • myeloproliferative syndrome (D47.1)
  • non-Hodgkin lymphoma (C82-C85)
  • plasma cell myeloma (C90.0-)
  • polycythemia vera (D45)

Inclusion Terms

  • Indolent systemic mastocytosis
  • Isolated bone marrow mastocytosis
  • Smoldering systemic mastocytosis
  • Systemic mastocytosis, with an associated hematological non-mast cell lineage disease (SM-AHNMD)

U.S. Hospital Utilization

  • An estimated 1,085 U.S. inpatient stays in 2023 included D47.02 among the documented diagnoses.
  • 105 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Tx of primary site (TOC entry)

a. Admission/Encounter for treatment of primary site ............................................................. 33

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.2.a
Tx of secondary site (TOC entry)

b. Admission/Encounter for treatment of secondary site .......................................................... 33

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.2.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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