D47.01 Cutaneous mastocytosis

✓ Billable ICD-10-CM 2026
Open D47.01 in Web App →

The ICD-10-CM code for Cutaneous mastocytosis is D47.01 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
D37-D48: Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48)
Category D47
14 codes (11 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to D47.01:

  • Mastocytosis › cutaneous (diffuse) (maculopapular)
  • Urticaria › pigmentosa
  • Mastocytoma (extracutaneous) › solitary
  • Telangiectasia, telangiectasis (verrucous) › macularis eruptiva perstans
Excludes1
Not coded here. These conditions should NOT be coded together with D47.01.
  • congenital (diffuse) (maculopapular) cutaneous mastocytosis (Q82.2)
  • congenital urticaria pigmentosa (Q82.2)
  • extracutaneous mastocytoma (D47.09)

Inclusion Terms

  • Diffuse cutaneous mastocytosis
  • Maculopapular cutaneous mastocytosis
  • Solitary mastocytoma
  • Telangiectasia macularis eruptiva perstans
  • Urticaria pigmentosa

U.S. Hospital Utilization

  • An estimated 270 U.S. inpatient stays in 2023 included D47.01 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

Tx of primary site (TOC entry)

a. Admission/Encounter for treatment of primary site ............................................................. 33

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.2.a
Tx of secondary site (TOC entry)

b. Admission/Encounter for treatment of secondary site .......................................................... 33

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section I.C.2.b

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

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Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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