D47.01 Cutaneous mastocytosis
The ICD-10-CM code for Cutaneous mastocytosis is D47.01 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Chapter
- 2: Neoplasms (C00-D49)
- Section
- D37-D48: Neoplasms of uncertain behavior, polycythemia vera and myelodysplastic syndromes (D37-D48)
- Category D47
- 14 codes (11 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to D47.01:
- Mastocytosis › cutaneous (diffuse) (maculopapular)
- Urticaria › pigmentosa
- Mastocytoma (extracutaneous) › solitary
- Telangiectasia, telangiectasis (verrucous) › macularis eruptiva perstans
Inclusion Terms
- Diffuse cutaneous mastocytosis
- Maculopapular cutaneous mastocytosis
- Solitary mastocytoma
- Telangiectasia macularis eruptiva perstans
- Urticaria pigmentosa
U.S. Hospital Utilization
- An estimated 270 U.S. inpatient stays in 2023 included D47.01 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
Tx of primary site (TOC entry)a. Admission/Encounter for treatment of primary site ............................................................. 33
Tx of secondary site (TOC entry)b. Admission/Encounter for treatment of secondary site .......................................................... 33
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026