Q99.811 Usher syndrome, type 1

The ICD-10-CM code for Usher syndrome, type 1 is Q99.811 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

17: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Section

Q90-Q99: Chromosomal abnormalities, not elsewhere classified (Q90-Q99)

Category Q99

13 codes (10 billable)

FY2026 Status

New code in FY2026

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q99.811:

• Syndrome › usher › type 1

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool