Q84.1 Congenital morphological disturbances of hair, not elsewhere classified

✓ Billable ICD-10-CM 2026
Open Q84.1 in Web App →

The ICD-10-CM code for Congenital morphological disturbances of hair, not elsewhere classified is Q84.1 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q80-Q89: Other congenital malformations (Q80-Q89)
Category Q84
10 codes (9 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q84.1:

  • Beaded hair (congenital)
  • Trichostasis spinulosa (congenital)
  • Ringed hair (congenital)
  • Monilethrix (congenital)
  • Woolly, wooly hair (congenital) (nevus)
  • Thrix annulata (congenital)
  • Twist, twisted › hair (congenital)
  • Pili › annulati or torti (congenital)
Excludes1
Not coded here. These conditions should NOT be coded together with Q84.1.
  • Menkes' kinky hair syndrome (E83.09)

Inclusion Terms

  • Beaded hair
  • Monilethrix
  • Pili annulati

U.S. Hospital Utilization

Q84.1 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

Get HCC Mappings, Clinical Summaries, and More

Access premium features including HCC risk adjustment, FDA drug indications, AI coding assistant, and comprehensive clinical context.

Start Free Trial