Q74.0 Other congenital malformations of upper limb(s), including shoulder girdle
The ICD-10-CM code for Other congenital malformations of upper limb(s), including shoulder girdle is Q74.0 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q65-Q79: Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)
- Category Q74
- 7 codes (6 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q74.0:
- Cleidocranial dysostosis
- Triphalangeal thumb
- Craniocleidodysostosis
- Sprengel's deformity (congenital)
- Megalodactylia (fingers) (thumbs) (congenital)
- Macrodactylia, macrodactylism (fingers) (thumbs)
- Accessory (congenital) › carpal bones
- Accessory (congenital) › navicular of carpus
Inclusion Terms
- Accessory carpal bones
- Cleidocranial dysostosis
- Congenital pseudarthrosis of clavicle
- Macrodactylia (fingers)
- Madelung's deformity
- Radioulnar synostosis
- Sprengel's deformity
- Triphalangeal thumb
U.S. Hospital Utilization
- An estimated 1,745 U.S. inpatient stays in 2023 included Q74.0 among the documented diagnoses.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026