Q74.0 Other congenital malformations of upper limb(s), including shoulder girdle

✓ Billable ICD-10-CM 2026
Open Q74.0 in Web App →

The ICD-10-CM code for Other congenital malformations of upper limb(s), including shoulder girdle is Q74.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q65-Q79: Congenital malformations and deformations of the musculoskeletal system (Q65-Q79)
Category Q74
7 codes (6 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q74.0:

  • Cleidocranial dysostosis
  • Triphalangeal thumb
  • Craniocleidodysostosis
  • Sprengel's deformity (congenital)
  • Megalodactylia (fingers) (thumbs) (congenital)
  • Macrodactylia, macrodactylism (fingers) (thumbs)
  • Accessory (congenital) › carpal bones
  • Accessory (congenital) › navicular of carpus

Inclusion Terms

  • Accessory carpal bones
  • Cleidocranial dysostosis
  • Congenital pseudarthrosis of clavicle
  • Macrodactylia (fingers)
  • Madelung's deformity
  • Radioulnar synostosis
  • Sprengel's deformity
  • Triphalangeal thumb

U.S. Hospital Utilization

  • An estimated 1,745 U.S. inpatient stays in 2023 included Q74.0 among the documented diagnoses.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

Get HCC Mappings, Clinical Summaries, and More

Access premium features including HCC risk adjustment, FDA drug indications, AI coding assistant, and comprehensive clinical context.

Start Free Trial