Q61.19 Other polycystic kidney, infantile type

The ICD-10-CM code for Other polycystic kidney, infantile type is Q61.19 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

17: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Section

Q60-Q64: Congenital malformations of the urinary system (Q60-Q64)

Category Q61

14 codes (11 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q61.19:

• Polycystic (disease) › kidney › infantile type NEC
• Cystic › kidney (congenital) › infantile type NEC
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › polycystic › infantile type NEC
• Polycystic (disease) › degeneration, kidney › autosomal recessive (infantile type) NEC
• Polycystic (disease) › kidney › autosomal recessive (childhood type) NEC
• Nephritis, nephritic (albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic) › polycystic › childhood type NEC
• Disease, diseased › kidney (functional) (pelvis) › polycystic › childhood type NEC
• Degeneration, degenerative › kidney › polycystic › infantile type (autosomal recessive) NEC

U.S. Hospital Utilization

• An estimated 775 U.S. inpatient stays in 2023 included Q61.19 among the documented diagnoses.
• 65 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)