Q56.1 Male pseudohermaphroditism, not elsewhere classified

The ICD-10-CM code for Male pseudohermaphroditism, not elsewhere classified is Q56.1 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Chapter

17: Congenital malformations, deformations and chromosomal abnormalities (Q00-QA0)

Section

Q50-Q56: Congenital malformations of genital organs (Q50-Q56)

Category Q56

6 codes (5 billable)

FY2026 Status

Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q56.1:

• Pseudohermaphroditism › male
• Pseudohermaphroditism › male › without gonadal disorder
• Rudimentary (congenital) › uterus › in male
• Karyotype › 46,XY › with streak gonads
• Pseudohermaphroditism › male › with › cleft scrotum

Inclusion Terms

• 46, XY with streak gonads
• Male pseudohermaphroditism NOS

U.S. Hospital Utilization

Q56.1 appeared in too few sampled U.S. inpatient stays in 2023 to report a national estimate (AHRQ suppresses counts of 10 or fewer) — a rare inpatient diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

• CMS — ICD-10-CM Official Code Set and Guidelines, FY2026
• CDC/NCHS — ICD-10-CM Files and Browser Tool
• AHRQ — HCUP National Inpatient Sample, Frequencies by Diagnosis Code (2016–2023)