Q43.1 Hirschsprung's disease
The ICD-10-CM code for Hirschsprung's disease is Q43.1 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q38-Q45: Other congenital malformations of the digestive system (Q38-Q45)
- Category Q43
- 11 codes (10 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q43.1:
- Macrocolon
- Aganglionosis (bowel) (colon)
- Hirschsprung's disease or megacolon
- Megacolon (acquired) (functional) (not Hirschsprung's disease) (in) › Hirschsprung's (disease)
- Megacolon (acquired) (functional) (not Hirschsprung's disease) (in) › congenital, congenitum (aganglionic)
- Dilatation › colon › congenital
- Ileus (bowel) (colon) (inhibitory) (intestine) › neurogenic › Hirschsprung's disease or megacolon
- Obstruction, obstructed, obstructive › intestine › neurogenic › Hirschsprung's disease or megacolon
Inclusion Terms
- Aganglionosis
- Congenital (aganglionic) megacolon
U.S. Hospital Utilization
- An estimated 6,130 U.S. inpatient stays in 2023 included Q43.1 among the documented diagnoses.
- 1,750 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026