Q40.0 Congenital hypertrophic pyloric stenosis

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Congenital hypertrophic pyloric stenosis is Q40.0 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q38-Q45: Other congenital malformations of the digestive system (Q38-Q45)
Category Q40
7 codes (6 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q40.0:

  • Pylorospasm (reflex) NEC › newborn
  • Achalasia (cardia) (esophagus) › pylorus
  • Pylorospasm (reflex) NEC › congenital or infantile
  • Spasm (s), spastic, spasticity › pylorus NEC › congenital or infantile
  • Obstruction, obstructed, obstructive › pylorus › congenital or infantile
  • Hypertrophy, hypertrophic › pylorus (adult) (muscle) (sphincter) › congenital or infantile
  • Constriction › pylorus (adult hypertrophic) › congenital or infantile
  • Constriction › pylorus (adult hypertrophic) › newborn

Inclusion Terms

  • Congenital or infantile constriction
  • Congenital or infantile hypertrophy
  • Congenital or infantile spasm
  • Congenital or infantile stenosis
  • Congenital or infantile stricture

U.S. Hospital Utilization

  • An estimated 4,035 U.S. inpatient stays in 2023 included Q40.0 among the documented diagnoses.
  • 3,400 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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