Q40.0 Congenital hypertrophic pyloric stenosis
The ICD-10-CM code for Congenital hypertrophic pyloric stenosis is Q40.0 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q38-Q45: Other congenital malformations of the digestive system (Q38-Q45)
- Category Q40
- 7 codes (6 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q40.0:
- Pylorospasm (reflex) NEC › newborn
- Achalasia (cardia) (esophagus) › pylorus
- Pylorospasm (reflex) NEC › congenital or infantile
- Spasm (s), spastic, spasticity › pylorus NEC › congenital or infantile
- Obstruction, obstructed, obstructive › pylorus › congenital or infantile
- Hypertrophy, hypertrophic › pylorus (adult) (muscle) (sphincter) › congenital or infantile
- Constriction › pylorus (adult hypertrophic) › congenital or infantile
- Constriction › pylorus (adult hypertrophic) › newborn
Inclusion Terms
- Congenital or infantile constriction
- Congenital or infantile hypertrophy
- Congenital or infantile spasm
- Congenital or infantile stenosis
- Congenital or infantile stricture
U.S. Hospital Utilization
- An estimated 4,035 U.S. inpatient stays in 2023 included Q40.0 among the documented diagnoses.
- 3,400 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026