Q27.9 Congenital malformation of peripheral vascular system, unspecified

✓ Billable ICD-10-CM 2026
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The ICD-10-CM code for Congenital malformation of peripheral vascular system, unspecified is Q27.9 (FY2026). It is a billable, claim-ready diagnosis code.

Classification

Section
Q20-Q28: Congenital malformations of the circulatory system (Q20-Q28)
Category Q27
14 codes (12 billable)
FY2026 Status
Stable since FY2024

Also Known As

ICD-10-CM Alphabetic Index entries that lead to Q27.9:

  • Distribution vessel, atypical
  • Agenesis › vein (s) (peripheral)
  • Agenesis › artery (peripheral)
  • Accessory (congenital) › blood vessels NEC
  • Anomaly, anomalous (congenital) (unspecified type) › vascular
  • Anomaly, anomalous (congenital) (unspecified type) › peripheral vascular system
  • Anomaly, anomalous (congenital) (unspecified type) › artery (peripheral)
  • Anomaly, anomalous (congenital) (unspecified type) › capillary

Inclusion Terms

  • Anomaly of artery or vein NOS

U.S. Hospital Utilization

  • An estimated 3,185 U.S. inpatient stays in 2023 included Q27.9 among the documented diagnoses.
  • 265 stays listed it as the principal diagnosis.

Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.

Official Coding Guidelines

POA indicator for congenital conditions/anomalies and Q00-Q99 exception

Congenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.

— ICD-10-CM Official Guidelines for Coding and Reporting, FY2026, Section III

Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026

References

Related Codes

Search all 70,000+ ICD-10-CM codes →
Reviewed by Prajwal Shrestha, CPC, CRC
Certified Professional Coder (CPC) and Certified Risk Adjustment Coder (CRC) · AAPC Member ID 01997614 · About · Editorial policy · Content last reviewed: 2025-10-01

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