Q26.8 Other congenital malformations of great veins
The ICD-10-CM code for Other congenital malformations of great veins is Q26.8 (FY2026). It is a billable, claim-ready diagnosis code.
Classification
- Section
- Q20-Q28: Congenital malformations of the circulatory system (Q20-Q28)
- Category Q26
- 10 codes (9 billable)
- FY2026 Status
- Stable since FY2024
Also Known As
ICD-10-CM Alphabetic Index entries that lead to Q26.8:
- Scimitar syndrome
- Hypoplasia, hypoplastic › vena cava (inferior) (superior)
- Anomaly, anomalous (congenital) (unspecified type) › venous return
- Agenesis › vena cava (inferior) (superior)
- Absence (of) (organ or part) (complete or partial) › vena cava (inferior) (superior), congenital
- Absence (of) (organ or part) (complete or partial) › superior vena cava, congenital
- Atresia, atretic › vena cava (inferior) (superior)
- Azygos › continuation inferior vena cava
Inclusion Terms
- Absence of vena cava (inferior) (superior)
- Azygos continuation of inferior vena cava
- Persistent left posterior cardinal vein
- Scimitar syndrome
U.S. Hospital Utilization
- An estimated 1,705 U.S. inpatient stays in 2023 included Q26.8 among the documented diagnoses.
- 130 stays listed it as the principal diagnosis.
Source: National Inpatient Sample (NIS), Healthcare Cost and Utilization Project (HCUP), Agency for Healthcare Research and Quality, 2016–2023. National survey-weighted estimates.
Official Coding Guidelines
POA indicator for congenital conditions/anomalies and Q00-Q99 exceptionCongenital conditions and anomalies Assign “Y” for congenital conditions and anomalies except for categories Q00- Q99, Congenital anomalies, which are on the exempt list. Congenital conditions are always considered present on admission.
Source: CMS — ICD-10-CM Official Guidelines for Coding and Reporting, FY2026